Search results for "Genetic Screens"

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Optimizing clinical exome design and parallel gene-testing for recessive genetic conditions in preconception carrier screening: Translational researc…

2019

Limited translational genomic research data have been reported on the application of exome sequencing and parallel gene testing for preconception carrier screening (PCS). Here, we present individual-level data from a large PCS program in which exome sequencing was routinely performed on either gamete donors (5,845) or infertile patients (8,280) undergoing in vitro fertilization (IVF) treatment without any known family history of inheritable genetic conditions. Individual-level data on pathogenic variants were used to define conditions for PCS based on criteria for severity, penetrance, inheritance pattern, and age of onset. Fetal risk was defined based on actual carrier frequency data accou…

MaleCancer ResearchGenetic ScreensHeredityGenetic LinkageMolecular biologyGenetic Carrier ScreeningGene Identification and AnalysisGene SequencingQH426-470BioinformaticsPathology and Laboratory MedicineTranslational Research Biomedical0302 clinical medicineSequencing techniquesMedicine and Health SciencesExomeDNA sequencingGenome SequencingChildExomeGenetics (clinical)Exome sequencing0303 health scienceseducation.field_of_studymedicine.diagnostic_testGenetic Carrier ScreeningGenomicsPenetranceX-Linked TraitsSex LinkageChild PreschoolMedical geneticsFemalePathogensResearch ArticleAdultmedicine.medical_specialtyHeterozygotePopulationGenes RecessiveBiology03 medical and health sciencesGenomic MedicineDirected Tissue DonationExome SequencingmedicineGeneticsHumansGenetic Predisposition to DiseaseGenetic TestingeducationEcology Evolution Behavior and Systematics030304 developmental biologyGenetic testingClinical GeneticsGenome HumanInfant NewbornBiology and Life SciencesInfantHuman geneticsResearch and analysis methodsMolecular biology techniquesInfertilityGenetics of DiseaseMutation030217 neurology & neurosurgeryPLoS Genetics
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2018

Drosophila melanogaster has been for over a century the model of choice of several neurobiologists to decipher the formation and development of the nervous system as well as to mirror the pathophysiological conditions of many human neurodegenerative diseases. The rare disease Friedreich’s ataxia (FRDA) is not an exception. Since the isolation of the responsible gene more than two decades ago, the analysis of the fly orthologue has proven to be an excellent avenue to understand the development and progression of the disease, to unravel pivotal mechanisms underpinning the pathology and to identify genes and molecules that might well be either disease biomarkers or promising targets for therap…

frataxinDrug Evaluation PreclinicalFriedreich’s ataxiaReviewLipid Metabolismdrug screensDisease Models AnimalOxidative Stressendoplasmic reticulumDrosophila melanogasterPhenotypeironFriedreich AtaxiaIron-Binding Proteinsmetal homeostasisAnimalsHumansGenetic Predisposition to DiseaseGene Silencinggenetic screensInternational journal of molecular sciences
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